Monckeberg’s sclerosis is a poorly understood condition associated with . Monckeberg’s sclerosis can coexist with atherosclerotic disease. Carlos Eduardo Barra Couri,1 Geruza Alves da Silva,1 José Antônio Baddini Martinez,1 Mönckeberg’s sclerosis (MS) is a degenerative and apparently .. The current concepts of the pathogenesis of Monckeberg-type arteriosclerosis. Mönckeberg sclerosis (MS) is a calcification of the me- dial layer of . ”Typical morphology of such calcifications in the early stages of the disease is linear de- posits along the . arteries in the absence of atherosclerotic plaque. Mayo Clin.

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Monckeberg’s sclerosis has been described in case reports, 3 9—12 as well as several case series. It may also result in “pulselessness.

Radiographic manifestations of Mönckeberg arteriosclerosis in the head and neck region

Support Center Support Center. Although one can argue about the possible role of upper airway obstruction in intensifying the local deposition of calcium in the soft tissue of the pharynx, the diagnosis of MS was arteriosclsrosis documented in this case.

Published online Dec Vascular ossification-calcification in metabolic syndrome, type 2 diabetes mellitus, chronic kidney disease, and calciphylaxis-calcific uremic arteriolopathy: However, it is likely that a secondary approach will have to be formulated for patients with widespread arterial calcification preventing arterial access altogether.

TelFaxude. Media calcification and intima calcification are distinct entities in chronic kidney disease. The frequency of upper limb predominant Monckeberg’s sclerosis is therefore unclear.

Mönckeberg medial calcific sclerosis | Radiology Reference Article |

Its pathophysiology is unclear, it is believed that the lesion will be produced by fatty degeneration of the smooth muscle cells of the middle layer, forming a mass artwriosclerosis undergoes a hyaline degeneration and then it becomes calcified.

Connective tissue and its heritable disorders: The pathogenesis and natural history of Monckeberg’s sclerosis are briefly discussed. Clinical and laboratory findings excluded any kind of rheumatologic disease such as dermatomyositis, scleroderma or systemic lupus erythematosus. Clin J Am Soc Nephrol, 3pp.

The femoral arteries appeared to be thickened and pulses were frail although there were no signs of acute limb ischemia. There are 2 theories to explain the described phenomenon: The results of oral cavity, thyroid, cardiopulmonary and abdominal examination were unremarkable.


Case report A year-old Brazilian woman was referred to the hospital with a year history of an moncoeberg size of the anterior portion of the neck associated with progressive exertional dyspnea, nighttime arteriosclersis and coughing, dysphagia of solids and daytime sleepiness.

Hypertension, 55pp. Monckeberg’s sclerosis stands among the differential diagnoses of vasculitis, however, its clinical relevance has been undervalued due to the low clinical impact attributed to it and the low reported incidence, being considered as a condition secondary to a process of deposit of inert calcium.

Monckeberg’s arteriosclerosis

Although it is important monckebeerg rule afteriosclerosis atherosclerotic disease in all patients with Monckeberg’s sclerosis, it is equally important to rule out medial calcification in patients planned for percutaneous angiography and intervention. Carotid artery stenosis Renal artery stenosis.

Medial vascular calcification revisited: Monckeberg’s sclerosis is a primary disease of the arteries. J Clin Endocrino Metab. Neck radiograph evidences grossly calcified areas of soft tissue in the topography of the oropharynx. At first believed to be a benign condition exclusively involving small-sized and medium-sized arteries, without thrombosis and luminal obstruction characteristic of atherosclerotic disease 4 this condition has now been associated with a multitude of systemic conditions, including atherosclerosis, arteriosclerosia kidney disease and hyperparathyroidism.

The development of calcification of the arteries is a normal process of aging; risk factors such as diabetes mellitus and chronic kidney disease are directly related to its progression. Extensive calcifications of the bilateral lingual and facial arteries are noted arrows as well as calcific plaques arterioscllerosis bilateral carotid tree area arrow heads.

National Center for Biotechnology InformationU. The explored arteries were much affected by a process of wall calcification, eliminating any possibility of revascularization.

Open in a separate window. Please review our privacy policy. This loss of elasticity can subsequently lead to systolic hypertension, left ventricular hypertrophy and impaired myocardial perfusion and ultimately increased cardiovascular risk.

Arterial intima and media calcification: N Engl J Med,pp. However, it can occur in pseudoxanthoma elasticum and idiopathic arterial calcification of infancy as a pathological condition, as well.

After repeated failures at negotiating a hydrophilic wire after successful sheath insertion; fluoroscopy revealed extensive calcification of radial and ulnar arteries extending up to the brachial artery. Wrteriosclerosis cause of medial calcinosis remains unclear, but some insights into the etiopathogenic process have been provided by isolated studies.


After a prolonged stay in the intensive care unit, the patient was transferred to aarteriosclerosis, where steroid clearing was started and she died 8 days later due to ventilatory failure, for which no confirmatory clinical necropsy was performed.

Additionally, our patient presented low bone mineral density, and this finding supports recent evidences showing nonckeberg between arterial calcification and osteoporosis[ 1415 ]. Bilateral calcifications associated with the carotid arteries superimposed on the soft tissue of the neck circles. It is from these data that many authors consider the process as a calciphylaxis or calcinosis that can occur concomitantly with endovascular fibrosis; however, for others, Monckeberg’s monckeberf is an advanced stage of arteriosclerosis without clear evidence to define that it is a completely independent condition.

The patient did not present any traditional risk factors associated with atherosclerosis.

Monckeberg’s arteriosclerosis – Wikipedia

The process of calcification, in some cases, is perceptible in radiographic study. We also thank the patient for giving us a written consent for publishing his case. Comparative histological study of atherosclerotic lesions and microvascular changes in amputated lower limbs of diabetic and non-diabetic patients. Calcifications are also seen in lateral view Monckeberf. Knowledge of the radiographic appearance of this calcification is clinically useful in developing a differential diagnosis.

He reported having noticed, about a year ago, the occurrence of small necrotic lesions at the end of the right toes, not associated with pain or another local symptom. Cardiovascular examination was essentially normal.

Vascular calcification is a common consequence of arferiosclerosis and is more frequent in patients with diabetes, dyslipidemia, genetic diseases, and diseases involving disturbances of calcium metabolism.

She attained menopause at the age of